Objective: To describe dentoalveolar findings in one pediatric patient with a very rare Carpenter syndrome or acrocephalopolysyndactyly type II, and using cone beam computed tomography (CBCT).
Case report: We found a syndromic oligodontia, upper canine transmigration, and an exceptional agenesis of four lateral incisors. We also described the fourth case in the literature of a single solitary lower incisor on the midline, and the first case ever illustrated on CBCT.
Conclusions: We proposed and illustrated the use of the system of progressive numbering of teeth on CBCT axial views to better understand complex dental clinical situations such as syndromic oligodontia.